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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Muscle fibrosis
Myoblasts
Alzheimer's disease
Alphavirus
Aggregate
PABPN1
Skeletal muscle
Mass spectrometry
Bile salt hydrolases
Myopathy
Epigenetics
Accelerometry
Akt
Gene replacement
AUTOPHAGY
Cross-bridge kinetics
Oculopharyngeal muscular dystrophy
Aav-U7
Neuromuscular junction NMJ
Intercellular communication
PABPN1 agregates
Annexin A2
Fibrosis
Thérapie génique
Dystrophin
Calcium
MUTATIONS
Pax7
Dysferlinopathy
Haploinsufficiency
Xenograft
AAV
DUX4
Omics
FAPs
Andermann syndrome
Metabolism
OPMD
Regulatory T cells
Dystrophie musculaire oculopharyngée
Triplet expansion disease
Muscle
ALS
Effector T cells
Inflammation
Satellite cells
DNA methylation
Transcriptomics
APOPTOSIS
ARN
Differentiation
Myosin
Lamins
Autologous
Myogenesis
Atrophy
Myopathies
Regenerative medicine
Ageing
BINDING SPECIFICITY
Satellite cell
RNA
Arbovirus
AAV vectors
Myoblast
GENE
Geriatric assessment
Autoimmune diseases
Gene therapy
Cell therapy
Adipose tissue
Neuromuscular disease
Functional genomics
DMD
Muscle stem cells
Anti-acetylcholine receptor antibodies
Dysferlin
Exon-skipping
Muscular dystrophy
Muscle strength
Human
Muscle dystrophy
Nuclear envelope
Pharyngeal muscle
Antisens oligonucleotides
Duchenne muscular dystrophy
Myotube
Antiserum
AChR antibodies
Anti-fibrotic pharmacotherapies
Aged
Biomarker
Myositis
Agrégats de PABPN1
Actin
2-D PAGE
FSHD
Regeneration
Sarcopenia
Amyotrophic Lateral Sclerosis